Interstitial Lung Disease

Conditions and Treatments

Interstitial lung disease (ILD) is a general term for a group of conditions that cause scarring, called fibrosis, or inflammation of the lungs and gradually interferes with breathing. The diagnosis and management of ILD is often complex, and requires input from doctors across several areas of expertise.

The UCSF Interstitial Lung Disease Program evaluates all forms of interstitial lung disease. The following is a list of some of these conditions:

• Acute Interstitial Pneumonia (AIP or Hamman-Rich Syndrome)
• Asbestosis
• Bronchiolitis
• Connective Tissue-related ILD
  • Myositis-related ILD
  • Rheumatoid arthritis-related ILD
  • Scleroderma-related ILD
  • Sjogren's syndrome-related ILD
  • Systemic Lupus Erythematosis-related ILD
  • Undifferentiated Connective Tissue Disease-related ILD
• Cryptogenic Organizing Pneumonia (COP)
• Desquamative Interstitial Pneumonia (DIP)
• Diffuse Alveolar Hemorrhage (DAH)
• Drug-related ILD
• Eosinophilic Pneumonia
• Familial Pulmonary Fibrosis
• Hypersensitivity Pneumonitis
• Idiopathic Pulmonary Fibrosis (IPF)
• Langerhan's Cell Histiocytosis (aka Eosinophilic granuloma or Histiocytosis X)
• Lymphangioleiomyomatosis (LAM)
• Lymphocytic Interstitial Pneumonia (LIP)
• Non-specific Interstitial Pneumonia (NSIP)
• Pulmonary Alveolar Proteinosis (PAP)
• Radiation fibrosis
• Respiratory Bronchiolitis-related ILD (RB-ILD)
• Sarcoidosis
• Silicosis
• Wegener's granulomatosis and other vasculitidies

Reviewed by health care specialists at UCSF Medical Center.
Last updated January 19, 2010