Treatment Heart & Vascular

Ebstein Anomaly
Treatments

If the deformity is severe at birth, it may require immediate surgery. In adults with milder cases, treatment may include medications or special procedures to manage arrhythmia. People with Ebstein anomaly should be prescribed antibiotics before surgery or dental procedures to protect against endocarditis.

If medication no longer controls symptoms or if the heart enlarges and loses efficiency, surgery may be required. The surgery may either repair the tricuspid valve or replace it with an artificial valve. It also may involve repairing any associated condition such as atrial septal defect.

If arrhythmia is present, radiofrequency ablation, a procedure in which a burst of energy destroys an abnormal electrical pathway in the heart, may be necessary. Rarely, a permanent pacemaker will be implanted.

Adults with Ebstein anomaly should be followed regularly by a cardiologist with a special interest in adult congenital heart disease. Yearly echocardiograms are necessary in all but the mildest cases.

UCSF Health medical specialists have reviewed this information. It is for educational purposes only and is not intended to replace the advice of your doctor or other health care provider. We encourage you to discuss any questions or concerns you may have with your provider.

Recommended reading

FAQ: Electrophysiology Study and Catheter Ablation

Find commonly asked questions regarding Electrophysiology Study and Catheter Ablation including, how long the procedure is, when to return to work and more.

FAQ: Implantable Cardioverter Defibrillators

Many people have questions about implantable cardioverter defibrillators (ICDs) — how they work and why a doctor might offer one as part of treatment.

Electrophysiology Procedure

An electrophysiology (EP) study is a test performed to assess the heart's electrical system or activity and is used to diagnose abnormal heartbeats. Learn more.

How the Heart Works

The heart is muscular and hollow, constantly pumping blood to deliver oxygen and nutrients to the body and is comprised of four compartments. Learn more.

Preparing for an EP Study

Before electrophysiology (EP) study or catheter ablation procedure, please use this list to prepare and ensure your visit is as comfortable as possible.

Seeking care at UCSF Health

Expand Map

    Share