Idiopathic Pulmonary Fibrosis
Two antifibrotic medications — nintedanib and pirfenidone — were approved in the fall of 2014 for use in idiopathic pulmonary fibrosis. While these medications are not a cure, they have both been shown to slow the decline of lung function over time.
Ongoing studies of other medications for IPF have shown initial promise, but need more research.
Pulmonary rehabilitation is a structured exercise and education program designed to increase endurance, strength, and exercise capacity, as well as to decrease fatigue and shortness of breath, for people with chronic lung disease, including people with IPF.
Additionally, it is important that any other medical problems that are associated with IPF are treated, such as gastroesophageal reflux disease (GERD) and pulmonary hypertension.
Finally, lung transplant may be an effective treatment option for some people with IPF.
UCSF Health medical specialists have reviewed this information. It is for educational purposes only and is not intended to replace the advice of your doctor or other health care provider. We encourage you to discuss any questions or concerns you may have with your provider.
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ILD Nutrition Manual
Nutrition Manual for Interstitial Lung Disease including, General Guidelines for Eating Healthy, Body Mass Index, Increasing Protein in Your Diet and more.
Patients living with interstitial lung disease (ILD) will find numerous resources listed here, offering information and support.
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Pulmonary Rehabilitation for ILD Patients
Pulmonary rehabilitation is a comprehensive program for lung disease patients whose symptoms are impacting their everyday activities. Learn more here.
Find Supplemental Oxygen Resources including, The Need for Supplemental Oxygen, Your Oxygen Equipment, Oxygen Safety, Traveling With Oxygen, and more.
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